Congenital Heart Disease Glossary

Amplatzer device

A self-centering device delivered percutaneously by catheter for closure of an atrial septal defect, a patent foramen ovale or a patent ductus arteriosus.

anomalous pulmonary venous connection

Pulmonary venous return to the right heart, which may be total or partial.

aortic arch anomalies
Abnormalities of the aortic arch and its branching. Note that left or right aortic arch is defined by the mainstem bronchus that is crossed by the descending thoracic aorta and does not refer to the side of the midline on which the aorta descends.
 
In left aortic arch (normal anatomic arrangement) the descending thoracic aorta crosses over the left mainstem bronchus; the innominate artery branching into the right carotid and right subclavian artery arises first, the left carotid artery second and the left subclavian artery third. Usually, the first aortic arch vessel gives rise to the carotid artery that is opposite to the side of the aortic arch (i.e. the right carotid artery in left aortic arch and the left carotid artery in right aortic arch).
 
The most important anomalies are listed below.
aortic override

see tetralogy of Fallot.

aortic valve-sparing ascending aortic replacement

see David operation.

aortic-left ventricular defect (tunnel)

Vascular connection between the aorta and the left ventricle resulting in left ventricular volume overload due to regurgitation from the aorta via the tunnel to the left ventricle.

aorto-pulmonary collateral

Abnormal arterial vessel arising from the aorta, providing blood supply to the pulmonary arteries. May be single or multiple, and small or large (see also MAPCA). May be associated with tetralogy of Fallot, pulmonary atresia or other complex cyanotic congenital heart disease.

aorto-pulmonary septal defect

see aorto-pulmonary window.

aorto-pulmonary window

A congenital connection between the ascending aorta and main pulmonary artery, which may be contiguous with the semi-lunar valves, or, less often, separated from them. Simulates the physiology of a large PDA, but requires a more demanding repair. syn. aorto-pulmonary septal defect.

arterial switch operation

see Jatene procedure.

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